ICD-10-CM CODE H91.90

Unspecified hearing loss, unspecified ear

H91.90 is a billable code used to specify a medical diagnosis of unspecified hearing loss, unspecified ear. The code is valid for the fiscal year 2021 for the submission of HIPAA-covered transactions. The ICD-10-CM code H91.90 might also be used to specify conditions or terms like abruzzo erickson syndrome, acquired hearing loss, alopecia, onychodysplasia, hypohidrosis, deafness ectodermal dysplasia, asymmetrical hearing loss, ataxia with deafness and intellectual disability syndrome, atherosclerosis, deafness, diabetes, epilepsy, nephropathy syndrome, etc

ICD-10: H91.90

Short Description: Unspecified hearing loss, unspecified ear
Long Description: Unspecified hearing loss, unspecified ear


The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Abruzzo Erickson syndrome
  • Acquired hearing loss
  • Alopecia, onychodysplasia, hypohidrosis, deafness ectodermal dysplasia
  • Asymmetrical hearing loss
  • Ataxia with deafness and intellectual disability syndrome
  • Atherosclerosis, deafness, diabetes, epilepsy, nephropathy syndrome
  • Bilateral congenital malformation of ears
  • Bilateral congenital malformation of external ears
  • Bilateral hearing loss
  • Bilateral microtia with deafness and cleft palate syndrome
  • Bilateral optic atrophy of eyes
  • Camptodactyly and tall stature with scoliosis and hearing loss syndrome
  • Caudal appendage deafness syndrome
  • Central nervous system calcification, deafness, tubular acidosis, anemia syndrome
  • Choanal atresia
  • Choanal atresia, hearing loss, cardiac defect, craniofacial dysmorphism syndrome
  • Choroideremia
  • Choroideremia with deafness and obesity syndrome
  • Chronic deafness
  • Combined visual and hearing impairment
  • Complete deafness
  • Congenital absence of abdominal muscle
  • Congenital anomaly of caudal vertebra
  • Congenital anomaly of subcutaneous tissue
  • Congenital atresia of nares
  • Congenital atresia of nasopharynx
  • Congenital atresia of pharynx
  • Congenital cleft hand
  • Congenital generalized lipodystrophy
  • Congenital hereditary facial paralysis with variable hearing loss syndrome
  • Congenital leukonychia
  • Congenital malposition of testis
  • Deaf blind hypopigmentation syndrome Yemenite type
  • Deafness and intellectual disability Martin Probst type syndrome
  • Deafness and myopia syndrome
  • Deafness symptom
  • Deafness, enamel hypoplasia, nail defect syndrome
  • Deafness, small bowel diverticulosis, neuropathy syndrome
  • Decreased hearing
  • Diabetes mellitus AND insipidus with optic atrophy AND deafness
  • Dysmorphism, short stature, deafness, disorder of sex development syndrome
  • Eighth cranial nerve finding
  • Erythrokeratodermia variabilis
  • Eyelid myoclonus with absences
  • Finding of ability to hear conversational voice
  • Finding of ability to hear conversational voice
  • Finding of ability to hear loud voice
  • Finding of ability to hear loud voice
  • Finding of ability to hear whisper
  • Finding of ability to hear whisper
  • Finding of type of voice production
  • Fountain syndrome
  • Genetic lipodystrophy
  • Hearing difficulty
  • Hearing disorder
  • Hearing for conversational voice impaired
  • Hearing for loud voice impaired
  • Hearing for voice impaired
  • Hearing for whisper impaired
  • Hearing loss
  • Hearing loss associated with syndrome
  • Hearing loss remits during vertigo attacks
  • Hearing problem
  • Hereditary hearing loss
  • Hereditary sensory and autonomic neuropathy with deafness and global delay
  • Hereditary sensory neuropathy
  • High frequency deafness
  • Kniest-Stickler dysplasia group
  • Knuckle pads
  • Knuckle pads, deafness AND leukonychia syndrome
  • Lactic acidosis
  • Lipodystrophy, intellectual disability, deafness syndrome
  • Low frequency deafness
  • Medication non-adherence due to hearing impairment
  • MEDNIK syndrome
  • Microtia
  • Mid frequency deafness
  • Mild acquired hearing loss
  • Mild to moderate hearing loss
  • Mitochondrial myopathy, lactic acidosis, deafness syndrome
  • Mixed conductive AND sensorineural hearing loss
  • Moderate acquired hearing loss
  • Myoclonus, cerebellar ataxia, deafness syndrome
  • Neonatal hearing loss
  • Nephropathy, deafness, hyperparathyroidism syndrome
  • Neural hearing loss
  • O/E – deaf
  • O/E – hearing
  • O/E – hearing
  • O/E – patient noted to be lip-reading
  • O/E – significantly deaf
  • O/E – slightly deaf
  • O/E – very deaf
  • Oculootoradial syndrome
  • Optic atrophy of left eye
  • Optic atrophy of right eye
  • Otospondylomegaepiphyseal dysplasia
  • Palmoplantar keratoderma with deafness syndrome
  • Parathyroid hyperplasia
  • Paresis of lower extremity
  • Partial deafness
  • Perception of hearing loss
  • Peripheral neuropathy, myopathy, hoarseness, hearing loss syndrome
  • Peripheral sensory neuropathy
  • Photogenic epilepsy
  • Photomyoclonus, diabetes mellitus, deafness, nephropathy and cerebral dysfunction
  • Polyneuropathy, hearing loss, ataxia, retinitis pigmentosa, cataract syndrome
  • Primary hyperparathyroidism
  • Profound acquired hearing loss
  • Prune belly syndrome
  • Prune belly syndrome with pulmonic stenosis, mental retardation and deafness
  • Pseudohermaphroditism
  • Retinitis pigmentosa-deafness syndrome
  • Retinitis pigmentosa-deafness-ataxia syndrome
  • Rubella deafness
  • Sensory neuropathy
  • Severe acquired hearing loss
  • Severe hearing loss
  • Spastic paraparesis
  • Spastic paraparesis and deafness
  • Spastic paraplegia, nephritis, deafness syndrome
  • Speech and language developmental delay due to hearing loss
  • Split foot
  • Split hand, split foot malformation with sensorineural hearing loss syndrome
  • Traumatic deafness
  • Traumatic deafness, non-occupational
  • Unable to hear conversational voice
  • Unable to hear loud voice
  • Unable to hear whisper
  • Undescended testicle
  • Upper frequency deafness
  • Usher syndrome type 1
  • Usher syndrome type 2
  • Voice associated with deafness
  • Weissenbacher-Zweymuller syndrome
  • X-linked hereditary sensory and autonomic neuropathy with deafness

 Diagnostic Related Groups

The ICD-10 code H91.90 is grouped in the following groups for version MS-DRG V38.0  applicable from 10/01/2020 through 09/30/2021.


 Convert H91.90 to ICD-9

  • 389.9 – Hearing loss NOS (Approximate Flag)
 Code Classification
  • Diseases of the ear and mastoid process (H60–H95)
    • Other disorders of ear (H90-H94)
      • Other and unspecified hearing loss (H91)

 Code History

  • FY 2016 – New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 – No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 – No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 – No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 – No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2021 – No Change, effective from 10/1/2020 through 9/30/2021

 Information for Patients

Hearing Disorders and Deafness

Also called: Hearing loss, Presbycusis

It’s frustrating to be unable to hear well enough to enjoy talking with friends or family. Hearing disorders make it hard, but not impossible, to hear. They can often be helped. Deafness can keep you from hearing sound at all.

What causes hearing loss? Some possibilities are

  • Heredity
  • Diseases such as ear infections and meningitis
  • Trauma
  • Certain medicines
  • Long-term exposure to loud noise
  • Aging

There are two main types of hearing loss. One happens when your inner ear or auditory nerve is damaged. This type is usually permanent. The other kind happens when sound waves cannot reach your inner ear. Earwax build-up, fluid, or a punctured eardrum can cause it. Treatment or surgery can often reverse this kind of hearing loss.

Untreated, hearing problems can get worse. If you have trouble hearing, you can get help. Possible treatments include hearing aids, cochlear implants, special training, certain medicines, and surgery.

NIH: National Institute on Deafness and Other Communication Disorders
  • Acoustic trauma (Medical Encyclopedia)
  • Age-related hearing loss (Medical Encyclopedia)
  • Audiometry (Medical Encyclopedia)
  • Ear examination (Medical Encyclopedia)
  • Hearing loss (Medical Encyclopedia)
  • Occupational hearing loss (Medical Encyclopedia)
  • Otosclerosis (Medical Encyclopedia)
  • Sensorineural deafness (Medical Encyclopedia)

[Learn More]

Nonsyndromic hearing loss Nonsyndromic hearing loss is a partial or total loss of hearing that is not associated with other signs and symptoms. In contrast, syndromic hearing loss occurs with signs and symptoms affecting other parts of the body.Nonsyndromic hearing loss can be classified in several different ways. One common way is by the condition’s pattern of inheritance: autosomal dominant (DFNA), autosomal recessive (DFNB), X-linked (DFNX), or mitochondrial (which does not have a special designation). Each of these types of hearing loss includes multiple subtypes. DFNA, DFNB, and DFNX subtypes are numbered in the order in which they were first described. For example, DFNA1 was the first type of autosomal dominant nonsyndromic hearing loss to be identified.The characteristics of nonsyndromic hearing loss vary among the different types. Hearing loss can affect one ear (unilateral) or both ears (bilateral). Degrees of hearing loss range from mild (difficulty understanding soft speech) to profound (inability to hear even very loud noises). The term “deafness” is often used to describe severe-to-profound hearing loss. Hearing loss can be stable, or it may be progressive, becoming more severe as a person gets older. Particular types of nonsyndromic hearing loss show distinctive patterns of hearing loss. For example, the loss may be more pronounced at high, middle, or low tones.Most forms of nonsyndromic hearing loss are described as sensorineural, which means they are associated with a permanent loss of hearing caused by damage to structures in the inner ear. The inner ear processes sound and sends the information to the brain in the form of electrical nerve impulses. Less commonly, nonsyndromic hearing loss is described as conductive, meaning it results from changes in the middle ear. The middle ear contains three tiny bones that help transfer sound from the eardrum to the inner ear. Some forms of nonsyndromic hearing loss, particularly a type called DFNX2, involve changes in both the inner ear and the middle ear. This combination is called mixed hearing loss.Depending on the type, nonsyndromic hearing loss can become apparent at any time from infancy to old age. Hearing loss that is present before a child learns to speak is classified as prelingual or congenital. Hearing loss that occurs after the development of speech is classified as postlingual.